Established Hemophilia Treatment Safety
Connect to well-established quality and safety
A process that uses multiple steps designed to purify recombinant factors, including
factor VIII (FVIII)1,2
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Phase 1
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Fermentation (expression of the gene)
- Continuous perfusion processing
- Creates a consistent environment for gene expression through a high degree of cell
culture control that goes beyond basic parameters (oxygen, pH, temperature)
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Phase 2
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Purification process
- The rFVIII molecule is separated from the host cells in multiple chromatographic
steps, including:
- Ion exchange chromatography, which separates rFVIII molecule from impurities
- Immunoaffinity chromatography, which separates rFVIII from most of the other proteins
- Solvent/detergent virus inactivation, which inactivates viruses without damaging
the structure of the rFVIII molecule
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Phase 3
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Formulation
- Formulated without albumin
- Final formulation stabilizes the rFVIII molecule using sucrose instead of albumin2
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- No animal proteins added
- No human proteins added during purification or to the final formulation*
CSL Behring’s patented processes in action during recombinant factor development1,2
Connect him to safety supported by clinical trials
Low rate of drug-related adverse events in minimally treated and previously untreated
patients
Twenty-nine of the 726 adverse events were assessed as related to Helixate FS (0.3%).
Adverse reactions in patients with frequency ≥4% (N=61):
- Skin and subcutaneous disorders, 16.4%
- Blood and lymphatic system disorders, 15%
- General disorders and administration site conditions, 6.6%
Low rate of drug-related adverse events in previously treated patients
Twenty-four of the 451 adverse events were assessed as related to Helixate FS (0.1%).
Adverse reactions in patients with frequency ≥4% (N=73):
- Skin and subcutaneous disorders, 8.2%
- General disorders and administration site conditions, 4.1%
Low incidence of inhibitor development
- In minimally treated and previously untreated patients, the incidence of inhibitor
development with Helixate FS was 15% (N=61)
- Based on studies from around the world, it is estimated that the incidence of inhibitor
development in patients with severe or moderately severe hemophilia A is between
20% and 33%3
- In previously treated patients, the incidence of new inhibitor development was 0%
(N=73)
- In the Joint Outcome Study, which was conducted to demonstrate the effectiveness
of routine prophylaxis for prevention of joint damage in children, the incidence
of new inhibitor development was 12.5% (N=65)
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*The baby hamster kidney cell line used to produce Helixate® FS is grown
in a culture medium that contains human plasma protein.
1. Data on file. CSL Behring LLC.
2. Freudenberg W, inventor; Behringwerke Aktiengesellschaft, assignee. Stabilized
factor VIII preparations. US Patent 5,565,427. October 15, 1996.
3. DiMichele D. Inhibitors in Hemophilia: A Primer. 4th ed. Montreal: World Federation
of Hemophilia; 2008. Treatment of Hemophilia; no 7.